A role for ITPA variants in the clinical course of pulmonary Langerhans' cell histiocytosis?
نویسندگان
چکیده
Interstitial lung diseases (ILD) comprise a number of clinical conditions, including sarcoidosis, pulmonary fibrosis and pulmonary Langerhans’ cell histiocytosis (PLCH; histiocytosis X). The diagnostic workup for the classification of ILD is often complicated and tedious. PLCH is characterised by the proliferation of Langerhans’ cells and their infiltration into pulmonary tissues. In disseminated LCH, additional tissues are affected. PLCH is strongly associated with smoking and the clinical outcome depends upon cessation of smoking [1].
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عنوان ژورنال:
- The European respiratory journal
دوره 36 3 شماره
صفحات -
تاریخ انتشار 2010